Kinsbourne syndrome Overview:
Kinsbourne Syndrome (also known as Opsoclonus Myoclonus) is a rare neurological disorder that usually affects infants and young children. The disorder is characterized by the sudden onset of brief, repeated, shock-like spasms of several muscles within the arms, legs, or entire body (polymyoclonus), an impaired ability to control voluntary movements (ataxia), and continual, involuntary, rapid eye movements in both horizontal and vertical directions (opsoclonus).
In approximately 50 percent of affected individuals, a malignant tumor, usually a tumor of embryonic nerve cells (neuroblastoma), is responsible for the symptoms associated with Kinsbourne Syndrome. In most other cases, Kinsbourne Syndrome may be due to a viral infection such as Coxsackievirus B3, poliovirus, or St. Louis encephalitis virus. Rarely, the disorder may result due to other underlying causes such as a tumor within the skull (intracranial tumors) or hydrocephalus, a condition in which inhibition of the normal flow of cerebrospinal fluid (CSF) and abnormal widening (dilatation) of the cerebral spaces of the brain (ventricles) causes accumulation of CSF in the skull and potentially increased pressure on brain tissue.
Opsoclonus Myoclonus syndrome:
Condition with involuntary muscle and eye movement. More detailed information about the symptoms, causes, and treatments of Opsoclonus Myoclonus is available below.
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